Familial congenital hepatic fibrosis: report of a family with three affected children.
نویسندگان
چکیده
Congenital hepatic fibrosis (CHF) is a developmental disorder of the biliary system, characterized by defective remodeling of the ductal plate. Herein a family of three children, from consanguineous parents, with minor thalassemia is presented who suffered from congenital hepatic fibrosis (CHF). Prompt diagnosis and appropriate treatment are necessary to avoid further complications in the affected patients.
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عنوان ژورنال:
- Acta medica Iranica
دوره 51 9 شماره
صفحات -
تاریخ انتشار 2013